Leber's optic atrophy is also known as:
- Leber's hereditary optic neuropathy (LHON),
- Optic atrophy,
- Leber's optic neuropathy, and
- Hereditary optic neuroretinopathy.
(These synonyms are mentioned for information but are not necessarily
included as separate entries in this glossary. Where multiple entries
are included, the synonym text links to its entry.)
Leber's optic atrophy is a rare hereditary disorder
characterised by rapid loss of central vision due to neuroretinal degeneration
(i.e. visual field testing shows an enlarging central scotoma).
This condition is most commonly diagnosed in young men, typically in
the age range 27-34 years.
Leber's optic atrophy is named after German Ophthalmologist,
Theodor Karl Gustav von Leber (1840 - 1917), who described this condition
More about Ophthalmology: This section includes short definitions
of many diseases, disorders, and conditions of the eyes and visual system.
For definitions of other terms in this category, choose from the list
to the left (but note that this is not a complete/exhaustive list).
Other related pages include the diagram
of the eye, and definitions
of parts of the eye, a description
of the human retina, and definitions
of parts of the retina, and the section of short definitions
of clinical and surgical procedures re. eyes and human visual system.
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